{"id":9465,"date":"2024-10-22T12:20:09","date_gmt":"2024-10-22T10:20:09","guid":{"rendered":"https:\/\/letscureacc.com\/?post_type=glossary&#038;p=9465"},"modified":"2024-10-22T12:20:14","modified_gmt":"2024-10-22T10:20:14","slug":"syndrome-de-beckwith-wiedemann-bws","status":"publish","type":"glossary","link":"https:\/\/letscureacc.com\/fr\/glossaryindex\/syndrome-de-beckwith-wiedemann-bws\/","title":{"rendered":"Syndrome de Beckwith-Wiedemann (BWS)"},"content":{"rendered":"\n<p>Le BWS r\u00e9sulte de modifications \u00e9pig\u00e9n\u00e9tiques ou de mutations g\u00e9n\u00e9tiques des g\u00e8nes r\u00e9gulant la croissance, notamment sur le chromosome 11p15. Cette r\u00e9gion contient des g\u00e8nes tels que IGF2 et H19, qui jouent un r\u00f4le crucial dans la prolif\u00e9ration cellulaire.<br>Les enfants atteints du BWS ont un risque accru de d\u00e9velopper des tumeurs, y compris un corticosurr\u00e9nalome, en particulier dans la petite enfance. Par cons\u00e9quent, une surveillance \u00e9troite est recommand\u00e9e pendant les huit premi\u00e8res ann\u00e9es de vie.<\/p>\n","protected":false},"excerpt":{"rendered":"<p>Le BWS r\u00e9sulte de modifications \u00e9pig\u00e9n\u00e9tiques ou de mutations g\u00e9n\u00e9tiques des g\u00e8nes r\u00e9gulant la croissance, notamment sur le chromosome 11p15. Cette r\u00e9gion contient des g\u00e8nes tels que IGF2 et H19, qui jouent un r\u00f4le crucial dans la prolif\u00e9ration cellulaire.Les enfants atteints du BWS ont un&#8230;<\/p>\n","protected":false},"author":416,"featured_media":0,"menu_order":0,"template":"","meta":{"give_campaign_id":0,"inline_featured_image":false,"footnotes":""},"glossary-categories":[],"glossary-tags":[],"class_list":["post-9465","glossary","type-glossary","status-publish","hentry"],"_links":{"self":[{"href":"https:\/\/letscureacc.com\/fr\/wp-json\/wp\/v2\/glossary\/9465","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/letscureacc.com\/fr\/wp-json\/wp\/v2\/glossary"}],"about":[{"href":"https:\/\/letscureacc.com\/fr\/wp-json\/wp\/v2\/types\/glossary"}],"author":[{"embeddable":true,"href":"https:\/\/letscureacc.com\/fr\/wp-json\/wp\/v2\/users\/416"}],"version-history":[{"count":0,"href":"https:\/\/letscureacc.com\/fr\/wp-json\/wp\/v2\/glossary\/9465\/revisions"}],"wp:attachment":[{"href":"https:\/\/letscureacc.com\/fr\/wp-json\/wp\/v2\/media?parent=9465"}],"wp:term":[{"taxonomy":"glossary-categories","embeddable":true,"href":"https:\/\/letscureacc.com\/fr\/wp-json\/wp\/v2\/glossary-categories?post=9465"},{"taxonomy":"glossary-tags","embeddable":true,"href":"https:\/\/letscureacc.com\/fr\/wp-json\/wp\/v2\/glossary-tags?post=9465"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}